OBJECTIVE: Evaluate clinical outcome of early cyclic intravenous pamidronate treatment in children with moderate-to-severe osteogenesis imperfecta (OI), commenced before three years of age. METHODS: A retrospective review of 17 patients with moderate-to-severe OI. Development, anthropometry, fracture …

Thirty years ago, in the summer of 1982, I was introduced to pediatric nursing during my internship in the Sophia Children’s Hospital, Academic Hospital Rotterdam (now Erasmus MC). One of my unforgettable patients was Dirk, a 24-year-old man with cystic fibrosis (CF), who spent his time in hospital in …

Doel: Op systematische wijze de werking van IMT onderzoeken bij COPD en CF patiënten. Methode: Voor deze studie is literatuur gezocht in PubMed, Cochrane, PEDro en Googlescholar met betrekking tot IMT bij COPD en CF. De volgende zoektermen zijn gehanteerd: Inspiratory muscle training - IMT, COPD, Cystic …

BACKGROUND: Chest physiotherapy is widely prescribed to assist the clearance of airway secretions in people with cystic fibrosis (CF). Positive expiratory pressure (PEP) devices provide constant back pressure to the airways during expiration. This may improve clearance by building up gas behind mucus …